Ọrịa Eisenmenger
Eisenmenget syndrome maobu Eisenmenger's syndrome bu usoro nke do na long-standing left-to-right cardiac shunt butere nke si na congenital heart defect nke na ebute pulmonary hypertension nakwa ntughari shunt na cyanotic right-to-left shunt. Maka mputa nke nnucha n'iji echocardiography N'oge na ndu mmadu mere Ka nsogbu obi nke na eto ruo Eisenmenger syndrome belata.[1].
Ọrịa Eisenmenger n'ime nne dị ime nwere ike ịkpata nnukwu nsogbu, [2] ọ bụ ezie na a kọọrọ ọmụmụ nke ọma. [3] Ọnwụ nne na-adị site na 30% ruo 60%, ma enwere ike ịkọwa ya na mgbaasị, ọbara na-akpụ akpụ na akwara na-aga ebe ndị dị anya, hypovolemia, ụkwara ọbara ma ọ bụ preeclampsia. Ọtụtụ ọnwụ na-ewere ọnọdụ ma ọ bụ n'ime izu mbụ mgbe amuchara. A ga-edina ụmụ nwanyị dị ime na-arịa ọrịa Eisenmenger n'ụlọ ọgwụ mgbe izu nke 20 nke ime gasịrị, ma ọ bụ n'oge ma ọ bụrụ na nsogbu ahụike emee.
Ihe ịrịba ama na mgbaàmà
[dezie | dezie ebe o si]Ihe ịrịba ama na mgbaàmà nke ọrịa Eisenmenger gụnyere ndị a: [4]
- Cyanosis (acha anụnụ anụnụ na akpụkpọ ahụ nke sitere na enweghị ikuku oxygen)
- Ọnụ ọgụgụ dị elu nke mkpụrụ ndụ ọbara uhie
- Mkpịsị aka na-afụli elu ma ọ bụ na-afọli elu (klọb)
- Ịda mbà (nke a makwaara dị ka syncope)
- Ọrịa obi
- Obi na-akụkarị
- Nsogbu ọbara ọgbụgba
- Ịkụ ụkwara ọbara
- Enweghị ígwè
- Mmetụta (endocarditis na oyi bara ya n'ahụ)
- Nsogbu akụrụ
- Ọrịa strok
- Mmiri na-agbanye n'ime mmiri (nke a na-adịghị ahụkebe) n'ihi mmụba nke Nri acid resorption na mmepụta na-adịghị mma [5]
- Nkume ọkụkọ
Otu n'ime nsogbu kachasị njọ na nke a na-ahụkarị nke ọrịa Eisenmenger bụ arrhythmia nke obi, ọkachasị supraventricular arrhythmias. A chọpụtakwara ihe dị ka 40% nke ndị ọrịa a chọpụtara na ha nwere ọrịa Eisenmenger nwere arrhythmias ndị a n'oge nyocha ECG. Arhythmias ndị a nwere ọdịnihu ka njọ n'etiti ndị ọrịa nwere ọrịa Eisenmenger, ma e jiri ya tụnyere ndị mmadụ n'ozuzu ha, ọ pụkwara ịbụ isi iyi nke ọnwụ obi mberede.[6]
Ihe Ndị Na-akpata ya
[dezie | dezie ebe o si]Ọtụtụ nkwarụ obi amụrụ nwere ike ịkpata ọrịa Eisenmenger, gụnyere nkwarụ atrial septal, nkwarụ ventricular septal, patent ductus arteriosus, na ụdị ọrịa obi dị mgbagwoju anya.[1]
Nnyocha
[dezie | dezie ebe o si]A na-ahụkarị nchọpụta nke ọrịa Eisenmenger site na Transhoracic echocardiography, nke na-eme ka ọ dịrị mfe ịmata na nyocha nke shunts, nkwarụ anatomical, na ọrụ ventricular. Mgbe a chọpụtara ya, ma ọ bụ n'ọnọdụ ụfọdụ nke nchọpụta na-enweghị nkwubi okwu, enwere ike iji catheter nke obi iji kwado nchọpụta ahụ ma nyochaa nrụgide ọbara nke akpa ume nke onye ọrịa, uru dị mkpa maka amụma na ọgwụgwọ.[6]
Ọ bụrụ na a chọpụta nkwarụ na-akpali akpali n'obi tupu ọ kpatara nnukwu ọbara mgbali elu nke akpa ume, enwere ike idozi ya site na ịwa ahụ, na-egbochi ọrịa ahụ.[7] Mgbe ọbara mgbali elu nke akpa ume zuru iji gbanwee ọbara na-agafe na nkwarụ ahụ, Otú ọ dị, a na-ewere maladaptation dị ka ihe a na-apụghị ịgbanwe agbanwe, na transplantation obi-akpa ume ma ọ bụ transplantation akpa ume na mmezi nke obi bụ naanị nhọrọ ọgwụgwọ.Mgbatị bụ nhọrọ ọgwụgwọ ikpeazụ na naanị maka ndị ọrịa nwere ọdịnihu na ogo ndụ. Oge na iru eru nke transplantation ka bụ mkpebi siri ike. Afọ 5 na afọ 10 dị n'agbata 70% na 80%, 50% na 70%, 30% na 50%, n'otu n'otu.[8][9][10] Ebe ọ bụ na nkezi ndụ nke ndị ọrịa mgbe a mịnyechara akpa ume dị ala dị ka 30% na afọ 5, ndị ọrịa nwere ọnọdụ ọrụ ezi uche dị na ya metụtara ọrịa Eisenmenger emeela ka ndụ dịkwuo mma site na nlekọta ahụike na-agbaso omenala ma e jiri ya tụnyere mịnye. [11]
A na-enyocha ọgwụ na usoro ọgwụgwọ dị iche iche maka ọbara mgbali elu nke akpa ume maka ọgwụgwọ nke mgbaàmà.[12] A na-atụ aro nzacha ikuku maka eriri intravenous maka ndị nwere ọrịa Eisenmenger ndị a kpọgara n'ụlọ ọgwụ iji belata ihe ize ndụ nke iwebata ikuku na mberede n'ime akwara n'ihi ohere dị ukwuu maka Embolism ikuku. Ọ bụrụ na a na-ewebata ikuku n'ime akwara ma na-agafe na ventricular septal defective n'ime ọbara, ọrịa strok nwere ike ime. [citation needed]
Ọgwụ ndị na-egbochi arrhythmic dị mkpa maka ọtụtụ ndị ọrịa nwere ọrịa Eisenmenger, dịka ihe akaebe na-egosi na ọnwụ mberede nke obi na-akpata arrhythmia nwere ike ịbụ isi ihe kpatara ọnwụ n'etiti ndị ọrịa nwere nsogbu ahụ. Usoro ọgwụgwọ ndị a na-achọkarị iweghachi ma nọgide na-enwe ụda sinus, mana ntinye aka a họọrọ ga-adabere na ọdịdị nke arrhythmia onye ọrịa.[6]
Okwu mmalite
[dezie | dezie ebe o si]Ọrịa Eisenmenger bụ nke Paul Wood kpọrọ aha [13] n'aha Victor Eisenmenger, onye mbụ kọwara [14] ọnọdụ ahụ na 1897.
- ↑ 1.0 1.1 (April 2009) "[Eisenmenger syndrome]" (in da). Ugeskrift for Laeger 171 (15): 1270–5. PMID 19416617. Kpọpụta njehie: Invalid
<ref>tag; name "pmid19416617" defined multiple times with different content - ↑ (2008) "PGE1 nebulisation during caesarean section for Eisenmenger's syndrome: a case report". J Med Case Rep 2 (1): 149. DOI:10.1186/1752-1947-2-149. PMID 18466628.
- ↑ (November 2006) "Pregnancy in the patient with Eisenmenger's syndrome". Mt. Sinai J. Med. 73 (7): 1033–6. PMID 17195894. Retrieved on 2008-12-20.
- ↑ Eisenmenger syndrome | Genetic and Rare Diseases Information Center (GARD) – an NCATS Program. rarediseases.info.nih.gov. Retrieved on 2021-10-25.
- ↑ Braunwald E. Heart Disease: A Textbook of Cardiovascular Medicine. P 1617-1618. Ann Intern Med 1998; 128:745-755
- ↑ 6.0 6.1 6.2 Diller (2007-02-27). "Pulmonary Vascular Disease in Adults With Congenital Heart Disease" (in en). Circulation 115 (8): 1039–1050. DOI:10.1161/CIRCULATIONAHA.105.592386. ISSN 0009-7322. PMID 17325254. Kpọpụta njehie: Invalid
<ref>tag; name ":0" defined multiple times with different content - ↑ Eisenmenger syndrome. NIH MedLine Plus (2010-02-05).
- ↑ Goerler H, Simon A, Gohrbandt B, et al. Heart-lung and lung transplantation in grown-up congenital heart disease: long-term single centre experience. Eur J Cardiothorac Surg. 2007;32(6):926–31. [PubMed]
- ↑ Waddell TK, Bennett L, Kennedy R, Todd TR, Keshavjee SH. Heart-lung or lung transplantation for Eisenmenger syndrome. J Heart Lung Transplant. 2002;21(7):731–7. [PubMed]
- ↑ Heart-lung transplantation for Eisenmenger syndrome: early and long-term results. Stoica SC, McNeil KD, Perreas K, Sharples LD, Satchithananda DK, Tsui SS, Large SR, Wallwork J Ann Thorac Surg. 2001 Dec; 72(6):1887-91.
- ↑ Beghetti (Mar 2009). "Eisenmenger Syndrome" (in en). Journal of the American College of Cardiology 53 (9): 733–740. DOI:10.1016/j.jacc.2008.11.025. PMID 19245962.
- ↑ (2008-06-05) "Eisenmenger Syndrome Treatment & Management".
- ↑ Wood (1958). "Pulmonary hypertension with special reference to the vasoconstrictive factor.". British Heart Journal 20 (4): 557–70. DOI:10.1136/hrt.20.4.557. PMID 13584643.
- ↑ Eisenmenger V. Die angeborenen Defekte der Kammerscheidewände des Herzens. The condition was first mentioned by Hippocrates, the Greek physician. Zeitschr Klin Med 1897;32(Supplement):1-28.